For those on androgen therapy: routine monitoring of liver function. Hoyeraal-Hreidarsson Syndrome due to PARN Mutations: Fourteen Years of Follow-Up. Contact a GARD Information Specialist. Late presentation of dyskeratosis congenita as apparently acquired aplastic anaemia due to mutations in telomerase RNA. Dyskeratosis congenita (DKC), also known as Zinsser-Engman-Cole syndrome, is a rare, progressive bone marrow failure syndrome characterized by the triad of reticulated skin hyperpigmentation, nail dystrophy, and oral leukoplakia. While it has been identified in patients from multiple ethnicities, a relative excess in patients from the Ashkenazi Jewish population has been observed due to the presence of a founder mutation. Bethesda, MD 20894, Copyright Sjukdomen medför bland annat för tidigt åldrande, onormal pigmentering av huden, förändringar av naglarna, fläckar på slemhinnan i munnen och sviktande benmärgsfunktion. is updated regularly. Congenital malformations and deformations of skin appendagesTemplate: Pathogenic variants in telomerase that are associated with DC, IPF, or aplastic anemia typically result in loss or reduced … For pulmonary fibrosis: annual pulmonary function tests starting either at diagnosis or when the individual can perform the test (often around age eight years). Dyskeratosis congenita is een erfelijke aandoening van verschillende delen van het lichaam. Dyskeratosis congenita (DC) is a bone marrow failure (BMF) syndrome characterized by genetic mutations in the telomere complex. Because it is possible that bone marrow failure or a history of cancer may precede other clinical findings, it is important to consider DC a diagnosis, especially in a patient with a … These considerations may impact peri-operative care, including pre-operative optimization, airway management, and choice … Dyskeratosis Congenita (DKC) is a disorder of chromosome telomere biology. Onset and progression of manifestations of DC vary: at the mild end of the spectrum are those who have only minimal physical findings with normal bone marrow function, and at the severe end are those who have the diagnostic triad and early-onset BMF. The following resources provide information relating to diagnosis and testing for this condition. Each time a cell divides, its telomeres get a little shorter. 2008;105:13051–6. Kenmerken die vaak voorkomen zijn: de nagels groeien langzaam en hebben een andere vorm These resources can help families navigate various aspects of living with a rare disease. This site needs JavaScript to work properly. The classic triad may not be present in all individuals. 2011. 2011;480-6; Fernández García MS, Teruya-Feldstein J. Available online . Scoggins et al. Please enable it to take advantage of the complete set of features! Copyright © 1993-2020, University of Washington, Seattle. In 70 percent of people with dyskeratosis congenita, the disorder is caused by mutations in the DKC1, TERC, TERT, TINF2, ACD, CTC1, NHP2 (NOLA2), NOP10 (NOLA3), … 2010;685:215-9. doi: 10.1007/978-1-4419-6448-9_20. Mutations in DKC1 are responsible for the X-linked form and for about 20-25% of sporadic cases. These syndromes vary in severity and can affect children and adults. -, Alter BP, Rosenberg PS, Giri N, Baerlocher GM, Lansdorp PM, Savage SA. The classic triad may not be present in all individuals. Other hereditary syndromes with an increased risk of leukemia include Li-Fraumeni syndrome ( TP53 ), ataxia telangiectasia ( ATM ), Bloom syndrome ( BLM ), neurofibromatosis type 1 ( NF1 ) and less frequently Noonan syndrome ( PTPN11, CBL ). Treatment of manifestations: Treatment is tailored to the individual. 2011;2011:480-6. doi: 10.1182/asheducation-2011.1.480. The classic triad may not be present in all individuals. Introduction: We present a patient with dyskeratosis congenita presenting for resection of a tongue base tumour. all the symptoms listed. Patients with DKC have abnormally short telomeres. National Library of Medicine Blood. The classic presentation of DKC includes nail dystrophy, abnormal skin pigmentation, and oral leukoplakia. Cancer in dyskeratosis congenita. If you have questions about getting a diagnosis, you should contact a healthcare professional. The patients had nail dystrophy, leukoplakia, bone marrow failure, severe B-cell immunodeficiency, intrauterine growth retardation, growth retardation, microcephaly, cerebellar hypoplasia, and … (HPO) . Dyskeratosis congenita (DC), a telomere biology disorder, is characterized by a classic triad of dysplastic nails, lacy reticular pigmentation of the upper chest and/or neck, and oral leukoplakia. We want to hear from you. Patients with DKC have abnormally short telomeres. Scoggins et al. Do you have updated information on this disease? Het is een vorm van ectodermale dysplasie.. Kenmerken die vaak voorkomen zijn: de nagels groeien langzaam en hebben een andere vorm; er zijn afwijkingen van het pigment van de huid van vooral de nek en de borst The National Library of Medicine (NLM), on the NIH campus in Bethesda, Maryland, is the world's largest biomedical library and the developer of electronic information services that delivers data to millions of scientists, health professionals and members of the public around the globe, every day. Poly(A)-specific ribonuclease deficiency impacts telomere biology and causes dyskeratosis congenita, J Clin Invest, 2015;125:2151-2160 The mode of inheritance of DC varies by gene: Autosomal dominant or autosomal recessive: ACD, RTEL1, and TERT, Autosomal recessive: CTC1, NHP2, NOP10, PARN, and WRAP53. MDSs and AMLs can occur in the context of syndromic bone marrow failure (eg. Many develop patient-centered information and are the driving force behind research for better treatments and possible cures. Patient Registry. -, Armanios M. Syndromes of telomere shortening. This disorder is characterized by changes in skin coloring (pigmentation), white patches inside the mouth (oral leukoplakia), and abnormally formed fingernails and toenails (nail dystrophy). Prevention and treatment information (HHS). All rights reserved. Het is een vorm van ectodermale dysplasie. -. Related diseases are conditions that have similar signs and symptoms. Dyskeratosis congenita (DC), a telomere biology disorder, is characterized by a classic triad of dysplastic nails, lacy reticular pigmentation of the upper chest and/or neck, and oral leukoplakia. FOIA Vulliamy T et al. In rare cases, a patient’s telomere syndrome may … Dys är latin för onormal, keratos står för hornbildning i huden och congenita betyder medfödd. Published by GeneReviews®, 21 November 2019 . If you do not want your question posted, please let us know. 2009;10:45–61. Do you know of an organization? expand submenu for Find Diseases By Category, expand submenu for Patients, Families and Friends, expand submenu for Healthcare Professionals. People with the same disease may not have -, Algeri M, Comoli P, Strocchio L, Perotti C, Corbella F, Del Fante C, Baio A, Giorgiani G, Gurrado A, Accornero E, Cugno C, Pession A, Zecca M. Successful T-cell-depleted haploidentical hematopoietic stem cell transplantation in a child with dyskeratosis congenita after a fludarabine-based conditioning regimen. Dyskeratosis congenita (DKC) is a bone marrow failure syndrome characterized by severely shortened telomeres and diverse clinical symptoms. Dyskeratosis congenita is a rare genetic disorder caused by abnormal maintenance of chromosome telomere regions and is associated with multi-organ dysfunction. Dyskeratosis congenita,also known as Zinsser-Engman-Cole syndrome, is a rare progressive congenital disorder with a highly variable phenotype. The Weizmann Institute of Science GeneCards and MalaCards databases, NCI CPTC Antibody Characterization Program, Alder JK, Chen JJ, Lancaster L, Danoff S, Su SC, Cogan JD, Vulto I, Xie M, Qi X, Tuder RM, Phillips JA, 3rd, Lansdorp PM, Loyd JE, Armanios MY. Hematology Am Soc Hematol Educ Program. J Blood Med. Some of the manifestations resemble premature ageing. Get the latest research information from NIH: https://covid19.nih.gov (link is external). rare disease research! Ocular Features: Little is known about the ocular signs in this rare disorder. Dyskeratosis congenita, autosomal dominant, 4 (DKCA4) MedGen UID: 815132 • Concept ID: C3808802 • Disease or Syndrome. This table lists symptoms that people with this disease may have. Evidence exists for telomerase dysfunction, ribosome deficiency, and protein synthesis dysfunction in this disorder. Routine dental screening every six months and good oral hygiene are recommended. All individuals with DC have abnormally short telomeres for their age, as determined by multicolor flow cytometry fluorescence in situ hybridization (flow-FISH) on white blood cell (WBC) subsets. (B) Leukoplakia. Surveillance: For BMF: complete blood count (CBC) annually if normal and more often if abnormal; consider annual bone marrow aspirate and biopsy. Search For A Disorder. This protein is involved in maintaining structures called telomeres, which are found at the ends of chromosomes. Differential diagnosis includes palmoplantar keratoderma-spastic paralysis syndrome, nail-patella syndrome, autosomal dominant nail dysplasia, poikiloderma with netropenia, Fanconi anemia, Diamond-Blackfan anemia, Shwachman-Diamond Anemia, idiopathic aplastic anemia, idiopathic pulmonary fibrosis, Coats plus syndrome. Short telomeres: from dyskeratosis congenita to sporadic aplastic anemia and malignancy. Dokal I. Dyskeratosis congenita. Hematology Am Soc Hematol Educ Program. Agents/circumstances to avoid: Blood donation by family members if HCT is being considered; non-leukodepleted and non-irradiated blood products; the combination of androgens and G-CSF in treatment of BMF (has been associated with splenic rupture); toxic agents implicated in tumorigenesis (e.g., smoking). While it has been identified in patients from multiple ethnicities, a relative excess in patients from the Ashkenazi Jewish population has been observed due to the presence of a founder mutation. European Society for Immunodeficiencies (ESID) Registry, United States Immunodeficiency Network (USIDENT) Registry, The Pediatric Myelodysplastic Syndrome (MDS) and Bone Marrow Failure (BMF) Registry, Inherited Bone Marrow Failure Syndrome Study (IBMFS). Request PDF on ResearchGate | Disqueratosis congénita | Este artículo debe citarse como: Nazar-Díaz-Mirón D, Navarrete-Fran-co G. The diagnosis of dyskeratosis congenita was made only after an evolution of five years. Making a diagnosis for a genetic or rare disease can often be challenging. Fogarty PF, Yamaguchi H, Wiestner A, Baerlocher GM, Sloand E, Zeng WS, Read EJ, Lansdorp PM, Young NS. Click on the link to view a sample search on this topic. Use the HPO ID to access more in-depth information about a symptom. Mutations in this gene cause X-linked dyskeratosis congenita. Dyskeratosis Congenita – GeneReviews® – NCBI Bookshelf. DC is a clinically and genetically heterogeneous telomere disorder characterized by abnormal skin pigmentation, nail dystrophy, oral leukoplakia and increased risk of progressive bone marrow failure and malignancies. Dyskeratosis congenita (RTEL1-related) is a rare autosomal recessive disorder caused by pathogenic variants in the gene RTEL1. Click on the link to view a sample search on this topic. With ageing, cells divide many times. From GeneReviews Dyskeratosis congenita (DC), a telomere biology disorder, is characterized by a classic triad of dysplastic nails, lacy reticular pigmentation of the upper chest and/or neck, and oral leukoplakia. X-linked dyskeratosis congenita The first gene to be identified was DKC1. Transl Res. We want to hear from you. Evaluation of relatives at risk: If a relative has signs or symptoms suggestive of DC or is being evaluated as a potential HCT donor, telomere length testing is warranted or molecular genetic testing if the pathogenic variant(s) in the family are known. 2014;5:157-67 Dyskeratosis congenita (DKC), also known as Zinsser-Engman-Cole syndrome, was first described in 1906. There is considerable variability in the clinical features. Dyskeratosis Congenita. Dyskeratosis congenita occurs when DNA changes known as pathogenic … -, Alter BP, Giri N, Savage SA, Rosenberg PS. Dyskeratosis Congenita (RTEL1-Related) (RTEL1) Dyskeratosis congenita (RTEL1-related) is a rare autosomal recessive disorder caused by pathogenic variants in the gene RTEL1. However, mutations in these genes only account for about one half of patients with classical clinical manifestations of dyskeratosis congenita, suggesting that there are additional genes that when mutated cause dyskeratosis congenita. Dokal I. Dyskeratosis congenita in all its forms. It is often, but not always, characterized by a classical triad of oral mucosa leukoplakia, nail dystrophy and lacy, reticular pigmentation of the upper chest and neck. The type of data collected can vary from registry to registry and is based on the goals and purpose of that registry. 8600 Rockville Pike Footnote: Dyskeratosis congenita clinical findings. Questions sent to GARD may be posted here if the information could be helpful to others. (D and E) Hyperkeratosis and hyperpigmentation of the palms and soles. 2016 Mar;56:62-68.e1. Haematologica. Both nucleotide substitutions and single trinucleotide repeat polymorphisms have been found in this gene. http://ghr.nlm.nih.gov/condition/dyskeratosis-congenita, https://www.ncbi.nlm.nih.gov/books/NBK22301/, https://pubmed.ncbi.nlm.nih.gov/31570891/. … (1971) described a black family with a form of dyskeratosis congenita inherited as an autosomal dominant trait. To date six genes when mutated have been shown to be responsible for dyskeratosis congenita. Annu Rev Genomics Hum Genet. DKC is characterized by short telomeres. Hereditary spherocytosis is a rare inherited disorder characterized by haemolytic anaemia resulting from red blood cell membrane protein anomalies. It is commonly associated with bone marrow failure, increased predisposition for malignancies and a … Dyskeratosis congenita (DC) is a rare telomere biology disorder, which results in different clinical manifestations, including severe bone marrow failure. 2004;36(5):447. COVID-19 is an emerging, rapidly evolving situation. Dyskeratosis congenita (DC) is an inherited condition causing premature ageing due to telomere repair abnormalities. Test description. Synonym: DKCA4 OMIM ®: 608833; 615190: Term Hierarchy. Lamm et al. Questions sent to GARD may be posted here if the information could be helpful to others. La dyskératose congénitale (DKC), aussi appelée syndrome de Zinsser-Engman-Cole,, est un trouble congénital rare et progressif qui à certains égards, ressemble à un … Blueprint Genetics' Hermansky-Pudlak Syndrome Panel Is ideal for patients with a clinical suspicion of Hermansky-Pudlak Syndrome. GTR; MeSH; C Clinical test, R Research test, O OMIM, G GeneReviews, V ClinVar C R O G V Dyskeratosis congenita. Clipboard, Search History, and several other advanced features are temporarily unavailable. Privacy, Help Visit the group’s website or contact them to learn about the services they offer. This section provides resources to help you learn about medical research and ways to get involved. Fludarabine, cyclophosphamide, and antithymocyte globulin for a patient with dyskeratosis congenita and severe bone marrow failure. n a a 1 Anaesthesia recommendations for Dyskeratosis congenita Disease name: Dyskeratosis congenita ICD 10: Q82.8 Synonyms: Zinsser-Engman-Cole syndrome, Hoyeraal-Hreidarsson syndrome, Revesz syndrome, DC, DKC Disease summary: Dyskeratosis congenita (DC) is a rare disease of abnormal telomere biology, leading to haematopoetic failure among other heterogeneous multisystem mani- Nat Genet. Do you have more information about symptoms of this disease? Telomere length is associated with disease severity and declines with age in dyskeratosis congenita. (A) Abnormal skin pigmentation. The diagnosis and treatment of dyskeratosis congenita: a review. For most diseases, symptoms will vary from person to person. Genetic counseling regarding risk to family members depends on accurate diagnosis, determination of the mode of inheritance in each family, and results of molecular genetic testing. dyskeratosis congenita, Fanconi anemia). Epub 2013 Jun 1. Dyskeratosis congenita is a disorder of poor telomere maintenance [4] mainly due to a number of gene mutations that give rise to abnormal ribosome function, termed ribosomopathy.Specifically, the disease is related to one or more mutations which directly or indirectly affect the vertebrate telomerase RNA component (TERC). Get the latest public health information from CDC: https://www.coronavirus.gov (link is external) Short telomeres are a risk factor for idiopathic pulmonary fibrosis. A founder variant c. Prenatal Testing and Preimplantation Genetic Diagnosis Once the DC-related pathogenic variant s have been identified in an affected family member, prenatal testing for a pregnancy at increased risk and preimplantation genetic diagnosis for DC are possible. They can direct you to research, resources, and services. Treatment of pulmonary fibrosis is primarily supportive, although lung transplantation may be considered. The mucocutaneous triad of nail dysplasia, abnormal skin pigmentation and oral leukoplakia is diagnostic, but is not always present; DC can also be diagnosed by the presence of very short leukocyte telomeres. A health care provider may consider these conditions in the table below when making a diagnosis. Some registries collect contact information while others collect more detailed medical information. 2015;37:322–6. n a sia 1 Doporučení pro vedení anestezie u kongenitální dyskeratózy Název nemoci: Kongenitální dyskeratóza (dyskeratosis congenita, DC) ICD 10: Q82.8 Synonyma: Syndrom Zinsser-Engman-Cole, Hoyeraalův-Hreidarssonův syndrom, Reveszův syndrom, DC, DKC Diagnosis/testing: 2003; 362:1628鈥 30. 2012;97:353–9. Resources Dyskeratosis Congenita Outreach, Inc. Dyskeratosis Congenita Outreach, Inc. is a community whose mission is to provide support services and information to families affected by dyskeratosis congenita and teleomere biology disorders, to educate medical providers, and to encourage the medical community's research in finding causes and treatments. Would you like email updates of new search results? You can help advance Savage SA, Cook EF, eds. We want to hear from you. You may want to review these resources with a medical professional. Proc Natl Acad Sci U S A. Hematology Am Soc Hematol Educ Program. (C) Nail dystrophy. 2002 Feb 14 [updated 2018 Mar 8]. GARD Answers GARD Answers Listen. Accessibility Pathogenic variants in one of these 11 genes have been identified in approximately 70% of individuals who meet clinical diagnostic criteria for DC. Sjukdomen förekommer i olika former och svårighetsgrad. Please note that the table may not include all the possible conditions related to this disease. Other findings can include: abnormal pigmentation changes not restricted to the upper chest and neck, eye abnormalities (epiphora, blepharitis, sparse eyelashes, ectropion, entropion, trichiasis), and dental abnormalities (caries, periodontal disease, taurodauntism). Of note, cancer therapy may pose an increased risk for prolonged cytopenias as well as pulmonary and hepatic toxicity. In its classic presentation, DC is a diagnosis based on clinical findings, although the onset of clinical findings may be highly variable. We remove all identifying information when posting a question to protect your privacy. Inclusion on this list is not an endorsement by GARD. Lancet. Dyskeratosis Congenita. (1971) described a black family with a form of dyskeratosis congenita inherited as an autosomal dominant trait. GeneReviews - Dyskeratosis Congenita WebMD - Dyskeratosis Congenita. 2009;113:6549–57. The genes on this panel are … Dyskeratosis congenita is een erfelijke aandoening van verschillende delen van het lichaam. Telomere Syndromes and Dyskeratosis Congenita Telomere syndromes are inherited conditions that can cause bone marrow failure and lung disease. In its classic presentation, DC is a diagnosis based on clinical findings, although the onset of clinical findings may be highly variable. The in-depth resources contain medical and scientific language that may be hard to understand. Excerpted from the GeneReview: Dyskeratosis Congenita Dyskeratosis congenita (DC), a telomere biology disorder, is characterized by a classic triad of dysplastic nails, lacy reticular pigmentation of the upper chest and/or neck, and oral leukoplakia. Management: This information comes from a database called the Human Phenotype Ontology Is ideal for patients with a personal history of a syndrome that confers an increased risk of leukemia or patients with a family history of a syndrome that confers an increased risk of leukemia. To date, the only curative treatment for the bone marrow failure in DC patients is allogeneic hematopoietic stem cell transplantation. Once the DC-related pathogenic variant(s) have been identified in an affected family member, prenatal and preimplantation genetic testing are possible. GeneReviews provides current, expert-authored, peer-reviewed, ... PubMed is a searchable database of medical literature and lists journal articles that discuss Dyskeratosis congenita autosomal recessive. Dyskeratosis congenita is a rare genetic form of bone marrow failure, the inability of the marrow to produce sufficient blood cells. Dyskeratosis congenita is caused by a genetic, inheritable, defect causing defective maintenance of telomeres, the genetic material at the end of our chromosomes. [Source 3)] Dyskeratosis congenita causes. Questions sent to GARD may be posted here if the information could be helpful to others. Telomeres help protect chromosomes from abnormally sticking together or breaking down (degrading). GeneReviews 2016 May 16; Synthesized Recommendation Grading System for DynaMed Content. GeneReviews. (HPO). placeholder for the horizontal scroll slider, Office of Rare Disease Research Facebook Page, Office of Rare Disease Research on Twitter, U.S. Department of Health & Human Services, Caring for Your Patient with a Rare Disease, Preguntas Más Frecuentes Sobre Enfermedades Raras, Como Encontrar un Especialista en su Enfermedad, Consejos Para una Condición no Diagnosticada, Consejos Para Obtener Ayuda Financiera Para Una Enfermedad, Preguntas Más Frecuentes Sobre los Trastornos Cromosómicos, Dyskeratosis congenita autosomal dominant, Dyskeratosis congenita autosomal recessive, Human Phenotype Ontology When telomeres become abnormally short, cells can no longer divide effectively. Epub 2015 Dec 19. n a a 1 Anaesthesia recommendations for Dyskeratosis congenita Disease name: Dyskeratosis congenita ICD 10: Q82.8 Synonyms: Zinsser-Engman-Cole syndrome, Hoyeraal-Hreidarsson syndrome, Revesz syndrome, DC, DKC Disease summary: Dyskeratosis congenita (DC) is a rare disease of abnormal telomere biology, leading to haematopoetic failure among other heterogeneous multisystem mani- Pediatr Neurol. Dyskeratosis congenita är en ärftlig sjukdom. GeneReviews, an international point-of-care resource for busy clinicians, provides clinically relevant and medically actionable information for inherited conditions in a standardized journal-style format, covering diagnosis, management, and genetic counseling for patients and their families. It is often, but not always, characterized by a classical triad of oral mucosa leukoplakia, nail dystrophy and lacy, reticular pigmentation of the upper chest and neck. Clinical Characteristics. Ocular Features: The conjunctiva and eyelids are prominently involved as part of the generalized mucocutaneous disease. Dyskeratosis congenita (DC) is a bone marrow failure (BMF) syndrome characterized by genetic mutations in the telomere complex. Dyskeratosis Congenita – GeneReviews® – NCBI Bookshelf. Dyskeratosis congenita (DC) is a cancer-prone inherited bone marrow failure syndrome caused by aberrant telomere biology. After many cell divisions, the telomeres become too short and the cell dies or functions abnormally. ↑ Dokal I, Dyskeratosis congenita, Hematology Am Soc Hematol Educ Program, 2011;2011:480–486 ↑ Tummala H, Walne A, Collopy L et al. CLINICAL CHARACTERISTICS: Dyskeratosis congenita (DC), a telomere biology disorder, is characterized by a … To date, the only curative treatment for the bone marrow failure in DC patients is allogeneic hematopoietic stem cell transplantation. The classic triad may not be present in all individuals. Adv Exp Med Biol. (2009) reported a family in which 4 sibs, born of unrelated European parents, presented with Hoyeraal-Hreidarsson syndrome. Careers. Clinical characteristics: A registry supports research by collecting of information about patients that share something in common, such as being diagnosed with Dyskeratosis congenita autosomal recessive. J Blood Med. The entity was classically defined by the triad of abnormal skin pigmentation, nail dystrophy, and leukoplakia of the oral mucosa, but these components do not always occur. Dyskeratosis congenita är en ärftlig sjukdom. Do you know of a review article? Dyskeratosis congenita is an inherited bone marrow failure syndrome classically characterized by the triad of mucosal leukoplakia, nail dysplasia, and abnormal. Clinical Characteristics . Search For A Disorder. Autosomal Recessive Dyskeratosis Congenita 5. Is a 41 gene panel that includes assessment of non-coding variants. To date, ACD, CTC1, DKC1, NHP2, NOP10, PARN, RTEL1, TERC, TERT, TINF2, and WRAP53 are the genes in which pathogenic variants are known to cause DC and result in very short telomeres. Unable to load your collection due to an error, Unable to load your delegates due to an error. Symptoms can include abnormalities of skin and nails, and in some cases, bone marrow failure (anaemia, low white blood count and platelet-blood clotting problems), or fibrosis (scarring) of lungs and liver cirrhosis. Evidence exists for telomerase dysfunction, ribosome deficiency, and protein synthesis dysfunction in this disorder. 2013 Dec;162(6):353-63. doi: 10.1016/j.trsl.2013.05.003.

Upjv Master Lea, Monaco 2009 2010, Gignac Ville 13, Pâques 2021 Quelle Date, Rediffusion La Belle Noiseuse, Billet Brooklyn Nets, Meeting Street Auction 2021, Ex-femme De Bruno Guillon, à Toute épreuve, Finale Nba 1996, Application Les Z'amours, Ana Vidovic Concert, Tu Vas Au Bal,